- Spinal Muscular Atrophy (SMA) and related syndromes:
	- Infantile spinal muscular atrophy, type I [Werdnig-Hoffman]
- Other inherited spinal muscular atrophy
- Progressive bulbar palsy of childhood [Fazio-Londe]
- SMA adult form
- SMA childhood form, type II
- Distal SMA
- SMA juvenile form, type III [Kugelberg-Welander]
- SMA scapuloperoneal form
 
- Systemic atrophies primarily affecting central nervous system in diseases classified elsewhere
- Primary disorders of muscles
- Paraneoplastic and neuropathy
	- Sensorial paraneoplastic neuropathy [Denny Brown]
 
- Hereditary motor and sensory neuropathy
	- Charcot-Marie-Tooth
- Déjerine-Sottas
- Refsum's disease
- Hereditary motor and sensory neuropathy, types I-IV
- Hypertrophic neuropathy of infancy
- Peroneal muscular atrophy (axonal type) (hypertrophic type)
- Roussy-Lévy syndrome
 
- Neuropathy in association with hereditary ataxia , such as Ataxia Telangectasia
- Idiopathic progressive neuropathy
- Inflammatory polyneuropathy
	- Guillain-Barré syndrome
- Acute (post-) infective polyneuritis
 
- Drug-induced/Alcoholic/Toxic Agent/Radiation induced polyneuropathy
- Serum neuropathy
- Polyneuropathy in infectious and parasitic diseases classified elsewhere:
	- diphtheria
- infectious mononucleosis
- leprosy
- Lyme disease
- mumps
- postherpetic
- syphilis, late
- congenital syphilis, late
- tuberculous
- Diabetic polyneuropathy
 
- Polyneuropathy in:
	- other endocrine and metabolic diseases
- neoplastic disease
- nutritional deficiency
- systemic connective tissue disorders
- other musculoskeletal disorders
- Uraemic neuropathy
 
INCLUDES: arthrogryposis multiplex congenita, metabolic myopathies
EXCLUDES: Dermatomyositis
